Información adicional

• Num_publicacion 72(1)
• Resumen_ingles

  The placental mesenchymal dysplasia (DMP) is a rare disease that affects the development of placental vascularization and conditions the appearance of liver hamartomas and blood disorders in newborns. In addition it is associated with Beckwith-Wiedemann syndrome (BWS) in 25% of the cases, sharing a common genetic origin. We report a case of both entities (DMP and BWS) in a male newborn, who developed not only liver hamartomas as described in the literature but also liver hemangiomas with positive marker Glut-1 as a new finding; this molecule is related to a better therapeutic response and long-term prognosis. The patient recieved treatment with propranolol with successfull reduction of the lesions size.

• Palabras_clave_ingles Dysplasia Placental Mesenchymal Beckwith Hemangiomas
• Todos_autores Á. Mula Antón, M.E. Llinares Riestra, J.M. Lloreda García¹, J.L. Fuster Soler
• autores listados Á. Mula Antón, M.E. Llinares Riestra, J.M. Lloreda García, J.L. Fuster Soler
• Correspondecia
  A. Mula Antón. Servicio de Pediatría. Hospital Universitario «Virgen de la Arrixaca». Ctra. Madrid-Cartagena, s/n. 30120 El Palmar (Murcia).
  Correo electrónico: fitoelmito@hotmail.com
• Titulo_ingles Hepatic hemangiomas and hamartomas in children with Beckwith-Wiedemann syndrome associated with placental mesenchymal dysplasia
• Centros_trabajo Unidad de Onco-Hematología Infantil. Servicio de Pediatría. Hospital Universitario «Virgen de la Arrixaca». El Palmar (Murcia). ¹Servicio de Pediatría. Hospital Universitario «Santa Lucía». Cartagena (Murcia)
• Publicado en Acta Pediatr Esp. 2014; 72(1): e11-e14
• copyright ©2014 Ediciones Mayo, S.A.
• Fecha recepcion 26/11/12
• Fecha aceptacion 15/01/13